Bouaiyda Ayoub, Ababou Mourad, Grine Ali, Jeddab Achraf, Andaloussi Med Rabie, Mounir Khalil, Jaafari Abdelhamid, Balkhi Hicham, Drissi Mohammed
Journal: Medpeer Publisher
ISSN: 3066-2737
Volume: 3
Issue: 6
Date of Publication: 2026/06/07
Gamma-sarcoglycanopathy is a rare genetic limb-girdle muscular dystrophy that presents significant anesthetic and obstetric challenges during pregnancy.
We report the case of a 30-year-old patient at 39 weeks of gestation with generalized muscle weakness graded at 2/5 who was admitted in labor.
Due to her inability to deliver vaginally, a cesarean delivery was indicated and successfully performed under spinal anesthesia.
The anesthetic block utilized a mixture of 0,5% isobaric bupivacaine, fentanyl, and morphine, allowing for a complication-free extraction and stable recovery.
Regional anesthesia seems to be the best option for myopathic patients to avoid the inherent risks of general anesthesia, such as difficult intubation and rhabdomyolysis.
A comprehensive preoperative evaluation remains crucial to optimize maternal and fetal safety in the absence of standardized management guidelines.
Gamma-sarcoglycanopathy, Pregnancy , Anesthetic Management
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