Dyke-Davidoff-Masson Syndrome Revealed by Refractory Epilepsy in a Young Adult: A Case Report

Authors

Mehdi Salmane, Abdallah Said, Alia Yassine Kassab, Lina Lasri, Firdaous Touarsa, Meryem Fikri

Journal Information

Journal: Medpeer Publisher

ISSN: 3066-2737

Volume: 3

Issue: 5

Date of Publication: 2026/05/27

DOI: 10.70780/medpeer.000QGSX

Abstract

Dyke-Davidoff-Masson syndrome (DDMS) is a rare neurological condition characterized by cerebral hemiatrophy associated with compensatory osseous hypertrophy. We report the case of a 24-year-old man presenting with refractory focal seizures and progressive left-sided weakness since childhood. Brain MRI demonstrated marked right cerebral hemiatrophy with ipsilateral ventricular dilatation, calvarial thickening, and hyperpneumatization of the frontal sinus, consistent with Dyke-Davidoff-Masson syndrome. This case highlights the characteristic imaging features of this rare entity and the importance of MRI in establishing the diagnosis.

Keywords

Dyke-Davidoff-Masson syndrome, Cerebral hemiatrophy, Refractory epilepsy, Hemiparesis.